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Case Report: Evans Syndrome in Lupus

Matthew J. Herrmann, MD, & Faizah Siddique, MD  |  Issue: March 2021  |  March 15, 2021


Matthew J. Herrmann, MDMatthew J. Herrmann, MD, is a recent rheumatology fellowship graduate from Loyola University Medical Center, Illinois. He is currently in practice at HonorHealth, Arizona.

Faizah Siddique, MDFaizah Siddique, MD, is an assistant professor of medicine in the Division of Rheumatology, Allergy, and Immunology at Loyola University Medical Center.

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References

  1. Aringer M, Costenbader K, Daikh D, et al. 2019 European League Against Rheumatism/American College of Rheumatology classification criteria for systemic lupus erythematosus. Arthritis Rheumatol. 2019 Sep;71(9):1400–1412.
  2. Costallat GL, Appenzeller S, Costallat LTL. Evans syndrome and systemic lupus erythematosus: Clinical presentation and outcome. Joint Bone Spine. 2012Jul;79(4):362–364.
  3. Jaime-Pérez JC, Aguilar-Calderón PE, Salazar-Cavazos L, et al. Evans syndrome: Clinical perspectives, biological insights and treatment modalities. J Blood Med. 2018 Oct;9:171–184. 
  4. Evans RS, Takahashi K, Duane RT, et al. Primary thrombocytopenic purpura and acquired hemolytic anemia; Evidence for a common etiology. AMA Arch Intern Med. 1951 Jan;87(1):48–65. 
  5. Karakantza M, Mouzaki A, Theodoropoulou M, et al. Th1 and Th2 cytokines in a patient with Evans’ syndrome and profound lymphopenia. Br J Haematol. 2000 Sep;110(4):968–970.
  6. Mendonca S, Srivastava S, Kapoor R, et al. Evans syndrome and its link with systemic lupus erythematosus. Saudi J Kidney Dis Transpl. 2016 Jan;27(1):147–149. 
  7. Lube GE, Ferriani MPL, Campos LMA, et al. Evans syndrome at childhood-onset systemic lupus erythematosus diagnosis: A large multicenter study. Pediatr Blood Cancer. 2016 Jul;63(7):1238–1243.
  8. Miano M. How I manage Evans syndrome and AIHA cases in children. Br J Haematol. 2016 Feb;172(4):524–534. 
  9. Michel M, Chanet V, Dechartres A, et al. The spectrum of Evans syndrome in adults: New insight into the disease based on the analysis of 68 cases. Blood. 2009 Oct;114(15):3167–3172. 
  10. Tkachenko O, Lapina S, Maslyansky A, et al. Relapsing Evans syndrome and systemic lupus erythematosus with antiphospholipid syndrome treated with bortezomib in combination with plasma exchange. Clin Immunol. 2019 Feb;199:44–46. 
  11. Serris A, Amoura Z, Canouï-Poitrine F, et al. Efficacy and safety of rituximab for systemic lupus erythematosus-associated immune cytopenias: A multicenter retrospective cohort study of 71 adults. Am J Hematol. 2018 Mar;93(3):424–429. 

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