Video: Every Case Tells a Story| Webinar: ACR/CHEST ILD Guidelines in Practice

An official publication of the ACR and the ARP serving rheumatologists and rheumatology professionals

  • Conditions
    • Axial Spondyloarthritis
    • Gout and Crystalline Arthritis
    • Myositis
    • Osteoarthritis and Bone Disorders
    • Pain Syndromes
    • Pediatric Conditions
    • Psoriatic Arthritis
    • Rheumatoid Arthritis
    • Sjögren’s Disease
    • Systemic Lupus Erythematosus
    • Systemic Sclerosis
    • Vasculitis
    • Other Rheumatic Conditions
  • FocusRheum
    • ANCA-Associated Vasculitis
    • Axial Spondyloarthritis
    • Gout
    • Psoriatic Arthritis
    • Rheumatoid Arthritis
    • Systemic Lupus Erythematosus
  • Guidance
    • Clinical Criteria/Guidelines
    • Ethics
    • Legal Updates
    • Legislation & Advocacy
    • Meeting Reports
      • ACR Convergence
      • Other ACR meetings
      • EULAR/Other
    • Research Rheum
  • Drug Updates
    • Analgesics
    • Biologics/DMARDs
  • Practice Support
    • Billing/Coding
    • EMRs
    • Facility
    • Insurance
    • QA/QI
    • Technology
    • Workforce
  • Opinion
    • Patient Perspective
    • Profiles
    • Rheuminations
      • Video
    • Speak Out Rheum
  • Career
    • ACR ExamRheum
    • Awards
    • Career Development
  • ACR
    • ACR Home
    • ACR Convergence
    • ACR Guidelines
    • Journals
      • ACR Open Rheumatology
      • Arthritis & Rheumatology
      • Arthritis Care & Research
    • From the College
    • Events/CME
    • President’s Perspective
  • Search

Case Report: Lymphocytic Vasculitis of the Central Nervous System

Gbemisola Olayemi, MD, Evangeline Scopelitis, MD, & Jerald M. Zakem, MD  |  Issue: January 2019  |  January 17, 2019

References

  1. Carolei A, Sacco S. Central nervous system vasculitis. Neurol Sci. 2003 May;24(suppl 1):S8–S10.
  2. Firestein G, Budd R, Gabriel SE, et al. (2012). Kelley’s Textbook of Rheumatology, 9th ed. Philadelphia: Saunders, an imprint of Elsevier.
  3. Harbitz F. Unknown forms of arteritis with special reference to their relation to syphilitic arteritis and periarteritis nodosa. Am J Med Sci. 1922;163:250–272.
  4. Cravioto H, Feigin I. Noninfectious granulomatous angiitis with a predilection for the nervous system. Neurology. 1959 Sep;9:599–609.
  5. Salvarani C, Brown RD Jr., Calamia KT, et al. Primary central nervous system vasculitis: Analysis of 101 patients. Ann Neurol. 2007 Nov;62(5):442–451.
  6. Sigal LH. The neurologic presentation of vasculitic and rheumatologic syndromes. A review. Medicine (Baltimore). 1987 May;66(3):157–180.
  7. van der Ven AJ, van Oostenbrugge RJ, Kubat B, Tervaert JW. Cerebral vasculitis after initiation antiretroviral therapy. AIDS. 2002 Nov 22;16(17):2362–2364.
  8. Kossorotoff M, Touzé E, Godon-Hardy S, et al. Cerebral vasculopathy with aneurysm formation in HIV-infected young adults. Neurology. 2006 Apr 11;66(7):1121–1122.
  9. Thomas L, Davidson M, McCluskey RT. Studies of PPLO infection. I. The production of cerebral polyarteritis by Mycoplasma gallisepticum in turkeys; the neurotoxic property of the Mycoplasma. J Exp Med. 1966 May 1;123(5):897–912.
  10. Outteryck O, Sénéchal O, Berteloot D, et al. [Cerebral vasculitis secondary to Varicella-Zoster virus infection]. Rev Neurol (Paris). 2005 Sep;161(8–9):836–839.
  11. Alexander JJ, Lasky AS, Graf WD. Stroke associated with central nervous system vasculitis after West Nile virus infection. J Child Neurol. 2006 Jul;21(7):623–625.
  12. Brannagan TH 3rd. Retroviral-associated vasculitis of the nervous system. Neurol Clin. 1997 Nov;15(4):927–944.
  13. Bhat G, Mathur DS, Saxena GN, et al. Granulomatous angiitis of the central nervous system associated with herpes zoster. J Assoc Physicians India. 2002 Jul;50:977–978.
  14. Nogueras C, Sala M, Sasal M, et al. Recurrent stroke as a manifestation of primary angiitis of the central nervous system in a patient infected with human immunodeficiency virus. Arch Neurol. 2002 Mar;59(3):468–473.
  15. Calabrese LH, Mallek JA. Primary angiitis of the central nervous system. Report of 8 new cases, review of the literature, and proposal for diagnostic criteria. Medicine (Baltimore). 1988 Jan;67(1):20–39.
  16. Birnbaum J, Hellmann DB. Primary angiitis of the central nervous system. Arch Neurol. 2009 Jun;66(6):704–709.
  17. Miller DV, Salvarani C, Hunder GG, et al. Biopsy findings in primary angiitis of the central nervous system. Am J Surg Pathol. 2009 Jan;33(1):35–43.
  18. Salvarani C, Brown RD Jr., Huston J 3rd, et al. Treatment of primary CNS vasculitis with rituximab: Case report. Neurology. 2014 Apr 8;82(14):1287–1288.
  19. Schmidley JW. (2000) Central Nervous System Angiitis. Boston: Butterworth-Heinemann.
  20. Berlit P. Diagnosis and treatment of cerebral vasculitis. Ther Adv Neurol Disord. 2010 Jan;3(1):29–42.
  21. Pomper MG, Miller TJ, Stone JH, et al. CNS vasculitis in autoimmune disease: MR imaging findings and correlation with angiography. AJNR Am J Neuroradiol. 1999 Jan;20(1):75–85.
  22. Calabrese LH, Dodick DW, Schwedt TJ, Singhal AB. Narrative review: Reversible cerebral vasoconstriction syndromes. Ann Intern Med. 2007 Jan 2;146(1):34–44.
  23. Alrawi A, Trobe JD, Blaivas M, Musch DC. Brain biopsy in primary angiitis of the central nervous system. Neurology. 1999 Sep 11;53(4):858–860.
  24. Calabrese LH, Furlan AJ, Gragg LA, Ropos TJ. Primary angiitis of the central nervous system: Diagnostic criteria and clinical approach. Cleve Clin J Med. 1992 May–Jun;59(3):293–306.
  25. Salvarani C, Brown RD Jr., Christianson TJ, et al. Mycophenolate mofetil in primary central nervous system vasculitis. Semin Arthritis Rheum. 2015 Aug;45(1):55–59.
  26. De Boysson H, Arquizan C, Guillevin L, Pagnoux C. Rituximab for primary angiitis of the central nervous system: Report of 2 patients from the French COVAC cohort and review of the literature. J Rheumatol. 2013 Dec;40(12):2102–2103.
  27. Salvarani C, Brown RD Jr., Calamia KT, et al. Efficacy of tumor necrosis factor alpha blockade in primary central nervous system vasculitis resistant to immunosuppressive treatment. Arthritis Rheum. 2008 Feb 15;59(2):291–296.
  28. Hajj-Ali R, Villa-Forte AI, Abou-Chebel A, et al. Long term outcome of patients with primary angiitis of the central nervous system (PACNS). Arthritis Rheum. 2000 Sep;43(suppl 9):S162.
  29. Elenein RG, Sharer LR, Cook SD, et al. A second case of Marburg’s variant of multiple sclerosis with vasculitis and extensive demyelination. Mult Scler. 2011 Dec;17(12):1531–1538.
  30. Bosche B, Dohmen C, Impekoven P, et al. Stroke after initiation of interferon‐beta treatment for relapsing–remitting disseminated white matter disease. Acta Neuro Scand. 2006 Jun;113(6);433–436.

Page: 1 2 3 4 5 6 7 | Single Page
Share: 

Filed under:ConditionsVasculitis Tagged with:central nervous system vasculitiscyclophosphamideMethylprednisolonePrimary Angiitis of the Central Nervous System

Related Articles

    Meet the Challenge of Primary CNS Vasculitis

    September 1, 2011

    Diagnosis and treatment of this rare and poorly understood condition

    Rheumatology Case Report: When Moyamoya Disease Mimicks Primary Central Nervous System Vasculitis

    November 16, 2015

    Case report: A 60-year-old Hispanic male with poorly controlled hypertension was sent from the primary care clinic for evaluation of malignant hypertension with a systolic blood pressure above 200 mmHg. His symptoms at the time of presentation included episodic confusion, worsening vision and an unsteady gait. A head computed tomography (CT) scan showed a subacute…

    7 Key Insights Into the Evaluation of Central Nervous System Vasculitis

    May 13, 2021

    Many a rheumatology consult has centered on a perplexing question: Does this patient have central nervous system (CNS) vasculitis? At the 2021 ACR State-of-the-Art Clinical Symposium, Rula Hajj-Ali, MD, FACP, professor of medicine and associate director of vasculitis care and research, Cleveland Clinic Lerner College of Medicine, discussed this topic in detail, providing a series…

    2014 ACR/ARHP Annual Meeting: Diagnosing PACNS and Its Mimics

    February 1, 2015

    Accurate diagnosis for primary angiitis of the central nervous system requires close scrutiny, team effort

  • About Us
  • Meet the Editors
  • Issue Archives
  • Contribute
  • Advertise
  • Contact Us
  • Copyright © 2025 by John Wiley & Sons, Inc. All rights reserved, including rights for text and data mining and training of artificial technologies or similar technologies. ISSN 1931-3268 (print). ISSN 1931-3209 (online).
  • DEI Statement
  • Privacy Policy
  • Terms of Use
  • Cookie Preferences