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Case Report: A Polyarteritis Nodosa Conundrum

Hannah Krebsbach, MD, Ileannette Robledo Vega, MD, Nirupa Patel, MD, & Nkechinyere Emejuaiwe, MD, MPH  |  Issue: March 2022  |  

The ACR and the Vasculitis Foundation recently published a new PAN guideline. For details, click here.

References

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  2. Adams TN, Zhang D, Batra K, Fitzgerald J. Pulmonary manifestations of large, medium, and variable vessel vasculitis. Respir Med. 2018 Dec;145:182–191.
  3. Hernández-Rodríguez J, Alba MA, Prieto-González S, Cid MC. Diagnosis and classification of polyarteritis nodosa. J Autoimmun. Feb-Mar 2014;48–49:84–89.
  4. de Boysson H, Guillevin L. Polyarteritis nodosa neurologic manifestations. Neurol Clin. 2019 May;37(2):345–357.
  5. De Virgilio A, Greco A, Magliulo G, et al. Polyarteritis nodosa: A contemporary overview. Autoimmun Rev. 2016 Jun;15(6):564–70.
  6. Karim MY, Miranda LC, Tench CM, et al. Presentation and prognosis of the shrinking lung syndrome in systemic lupus erythematosus. Semin Arthritis Rheum. 2002 Apr;31(5):289–298.
  7. Pillai S, Mehta J, Levin T, et al. Shrinking lung syndrome presenting as an initial pulmonary manifestation of SLE. Lupus. 2014 Oct;23(11):1201–1203.
  8. Duron L, Cohen-Aubart F, Diot E, et al. Shrinking lung syndrome associated with systemic lupus erythematosus: A multicenter collaborative study of 15 new cases and a review of the 155 cases in the literature focusing on treatment response and long-term outcomes. Autoimmun Rev. 2016 Oct;15(10):994–1000.
  9. Scirè CA, Caporali R, Zanierato M, et al. Shrinking lung syndrome in systemic sclerosis. Arthritis Rheum. 2003 Oct;48(10):2999–3000.
  10. Tavoni A, Vitali C, Cirigliano G, et al. Shrinking lung in primary Sjögren’s syndrome. Arthritis Rheum. 1999 Oct;42(10):2249–2254.
  11. Smyth H, Flood R, Kane D, et al. Shrinking lung syndrome and systemic lupus erythematosus: a case series and literature review. QJM. 2018 Dec 1;111(12):839–843.
  12. Allan SG, Towla HM, Smith CC, et al. Painful brachial plexopathy: An unusual presentation of polyarteritis nodosa. Postgrad Med J. 1982 May;58(679):311–313.
  13. Cordero Sánchez M, Calvo Arenillas JI, Gutierrez DA, et al. Cervical radiculopathy: A rare symptom of giant cell arteritis. Arthritis Rheum. 1983 Feb;26(2):207–209.
  14. Feinberg JH, Radecki J. Parsonage-turner syndrome. HSS J. 2010 Sep;6(2):199–205.
  15. Borrell H, Narváez J, Alegre JJ, et al. Shrinking lung syndrome in systemic lupus erythematosus: A case series and review of the literature. Medicine (Baltimore). 2016 Aug;95(33):e4626.

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