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Case Report: Could Myocarditis + Shortness of Breath = EGPA?

Ambreesh Chawla, MD, Ashwini Komarla, MD, & Sujatha Vuyyuru, MD  |  Issue: August 2019  |  August 16, 2019


Ambreesh Chawla, MD, is a first-year rheumatology fellow at the University of Central Florida College of Medicine, Orlando, Fla. His clinical interests include vasculitis and connective tissue disease-related ILD.

Ashwini Komarla, MD, is a rheumatologist at the Orlando VA Medical Center. She is an assistant program director for the UCF/VA Rheumatology Fellowship Program.

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Sujatha Vuyyuru, MD, is the department chief of rheumatology at the Orlando VA Medical Center. She is the program director for the UCF/VA Rheumatology Fellowship Program.

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  4. Churg A. Pulmonary angiitis and granulomatosis revisited. Hum Pathol. 1983 Oct;14(10):868–883.
  5. Conron M, Beynon HL. Churg-Strauss syndrome. Thorax. 2000 Oct;55(10):870–877.
  6. Masi AT, Hunder GG, Lie JT, et al. The American College of Rheumatology 1990 criteria for the classification of Churg-Strauss syndrome (allergic granulomatosis and angiitis). Arthritis Rheum. 1990 Aug;33(8):10941–100.
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  8. Wechsler ME, Akuthota P, Jayne D, et al. Mepolizumab or placebo for eosinophilic granulomatosis with polyangiitis. N Engl J Med. 2017 May 18;376(20):1921–1932.
  9. Cottin V, Bel E, Bottero P, et al. Revisiting the systemic vasculitis in eosinophilic granulomatosis with polyangiitis (Churg-Strauss): A study of 157 patients by the Groupe d’Etudes et de Recherche sur les Maladies Orphelines Pulmonaires and the European Respiratory Society Taskforce on eosinophilic granulomatosis with polyangiitis (Churg-Strauss). Autoimmun Rev. 2017 Jan;16(1):1–9.
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  15. Corradi D, Maestri R, Facchetti F. Postpartum Churg-Strauss syndrome with severe cardiac involvement: Description of a case and review of the literature. Clin Rheumatol. 2009 Jun;28(6):739–743.
  16. Groh M, Pagnoux C, Baldini C, et al. Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) Consensus Task Force recommendations for evaluation and management. Eur J Intern Med. 2015 Sep;26(7):545–553.
  17. Guillevin L, Lhote F, Gayraud M, et al. Prognostic factors in polyarteritis nodosa and Churg-Strauss syndrome. A prospective study in 342 patients. Medicine (Baltimore). 1996 Jan;75(1):17–28.
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