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Fibrotic Diseases of the Retroperitoneum & Skin, & Rare Scleroderma Mimics

  |  Issue: January 2018  |  

“Aggressive physical therapy can be helpful as well, because patients frequently complain of a limited range of motion in their shoulders and neck,” said Dr. Hummers.

Susan Bernstein is a freelance journalist based in Atlanta.

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References

  1. Khosroshahi A, Carruthers MN, Stone JH, et al. Rethinking Ormond’s disease: “Idiopathic” retroperitoneal fibrosis in the era of IgG4-related disease. Medicine (Baltimore). 2013 Mar;92(2):82–91.
  2. Wallace ZS, Deshpande V, Mattoo H, et al. IgG4-related disease: Clinical and laboratory features in one hundred and twenty-five patients. Arthritis Rheumatol. 2015 Sep;67(9):2466–2475.
  3. Mazori DR, Femia AN, Vleugels RA. Eosinophilic fasciitis: An updated review on diagnosis and treatment. Curr Rheumatol Rep. 2017 Nov;19(12):74.
  4. Lakhanpal S, Ginsburg WW, Michet CJ, et al. Eosinophilic fasciitis: Clinical spectrum and therapeutic response in 52 cases. Semin Arthritis Rheum. 1988 May;17(4):221–231.
  5. Morgan ND, Hummers LK. Scleroderma mimickers. Curr Treatm Opt Rheumatol. 2016 Mar;2(1):69–84.
  6. Eckes B, Wang F, Moinzadeh P, et al. Pathophysiological mechanisms in sclerosing skin diseases. Front Med (Lausanne). 2014;4:120.
  7. Blum M, Wigley FM, Hummers LK. Scleromyxedema: A case series highlighting long-term outcomes of treatment with intravenous immunoglobulin (IVIG). Medicine (Baltimore). 2008 Jan;87(1):10-20.
  8. Rongioletti F, Kaiser F, Cinotti E, et al. Scleredema: A multicentre study of characteristics, comorbidities, course and therapy in 44 patients. J Eur Acad Dermatol Venereol. 2015 Dec;29(12):2399–2404.

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