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An official publication of the ACR and the ARP serving rheumatologists and rheumatology professionals

Vasculitis

Case Reports: Mimics of Polyarteritis Nodosa

Shane Murray, BMBS, RhMSUS, Zhe Ran Duan, MD, PhD, & Daniel DeMizio, MD  |  

When polyarteritis nodosa isn’t PAN: Two cases of mimics, segmental arterial mediolysis (SAM) & vascular Ehlers-Danlos syndrome (vEDS), are explored.

Case Report: Pulmonary Artery Stenosis Secondary to Granulomatosis with Polyangiitis

Sambhawana Bhandari, MD, & Colin Diffie, MD  |  

This report presents a rare case of bilateral pulmonary artery stenosis secondary to granulomatosis with polyangiitis, underscoring the importance of recognizing large-vessel involvement as a potential manifestation of AAV; it also includes a narrative review analyzing eight previously reported cases.

Key Research in Vasculitis Encapsulated

Philip Seo, MD, MHS  |  

Summaries of selected research abstracts on the assessment & management of systemic vasculitis from ACR Convergence 2024.

Case Report: Giant Cell Arteritis Presenting with Scalp Necrosis

Jude Al Qaqaa, MD, Vladimir Falb, DO, & Kaitlyn Buzard, DO  |  

Giant cell arteritis (GCA), is an inflammatory vasculitis that involves large- and mediumsized arteries, most commonly the cranial branches of the carotid artery.1 It is seen in individuals 50 years and older.1 The most typical manifestation is new-onset headache with scalp tenderness and jaw claudication. 2 The most feared complication associated with GCA is permanent…

ACR Image Competition 2024 Results, Part 1—Best Overall

Rachel Guess, MD  |  

For the 2024 Image Competition, the ACR sought images representing a diverse range of patients with educational or remarkable manifestations of pediatric rheumatic diseases, including autoimmune, inflammatory, infectious and malignant drivers of pediatric rheumatic disease. Here, we showcase the images selected as Best Overall. Cavitary Lung Nodules with Sinus & Skin Disease in Pediatric ANCA-Associated…

Case Report: Uncommon Complications in ANCA-Associated Vasculitis

Logan Oliver, MD, & Jason J. Weiner, MD, FACP, FACR  |  

Anti-neutrophil cytoplasmic antibody (ANCA) associated vasculitis is a rare autoimmune condition characterized by inflammation of small- and medium-sized vessels. ANCA-associated vasculitis can lead to multisystem organ complications, including life-threatening pulmonary hemorrhage, renal failure and death. We present a case of ANCA-associated vasculitis complicated by complement-mediated thrombotic microangiopathy (c-TMA). Of the rheumatic diseases, systemic lupus erythematosus…