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New Classification Criteria Describe Several Hereditary Fevers

Larry Beresford  |  

The criteria developed in this way also received cross-sectional validation.

The real advance of this approach has been to come up with criteria combining clinical manifestations with genotypes, with a new emphasis on molecular analysis, in trying to clarify these conditions.

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Larry Beresford is a medical journalist in Oakland, Calif.

References

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  1. Gattorno M, Hofer M, Federici S, et al. Classification criteria for autoinflammatory recurrent fevers. Ann Rheum Dis. 2019 Aug; 78(8):1025–1032.
  2. De Benedetti F, Gattorno M, Anton J, et al. Canakinumab for the treatment of autoinflammatory recurrent fever syndromes. N Engl J Med. 2018 May; 378(20):1908–1919.

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